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Exagamglogene autotemcel

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417:(EMA) adopted a positive opinion, recommending the granting of a conditional marketing authorization for the medicinal product Casgevy, intended for the treatment of transfusion‑dependent β‑thalassemia and sickle cell disease. As Casgevy is an advanced therapy medicinal product, the CHMP positive opinion is based on an assessment by the Committee for Advanced Therapies. The applicant for this medicinal product is Vertex Pharmaceuticals (Ireland) Limited. Exagamglogene autotemcel was approved for medical use in the European Union in February 2024. 373:
prior to screening. The primary efficacy outcome was freedom from severe vaso-occlusive crisis episodes for at least twelve consecutive months during the 24-month follow-up period. A total of 44 participants were treated with exagamglogene autotemcel. Of the 31 participants with sufficient follow-up time to be evaluable, 29 (93.5%) achieved this outcome. All treated participants achieved successful engraftment with no participants experiencing graft failure or
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myeloablative conditioning (high-dose chemotherapy), a process that removes cells from the bone marrow so they can be replaced with the modified cells in exagamglogene autotemcel. The modified blood stem cells are transplanted back into the recipient where they engraft (attach and multiply) within the bone marrow and increase the production of fetal hemoglobin (HbF), a type of hemoglobin that facilitates oxygen delivery.
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The gene therapy is made from the recipient's own blood stem cells, which are modified, and are given back as a one-time, single-dose infusion as part of a hematopoietic (blood) stem cell transplant. Prior to treatment, the recipient's own stem cells are collected, and then the recipient must undergo
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The safety and effectiveness of exagamglogene autotemcel were evaluated in an ongoing single-arm, multi-center trial in adult and adolescent participants with sickle cell disease. Participants had a history of at least two protocol-defined severe vaso-occlusive crises during each of the two years
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The treatment was approved in the United Kingdom for the treatment of sickle cell disease and transfusion-dependent beta thalassemia in November 2023. It was approved in the United States for the treatment of sickle cell disease in December 2023 and for the treatment of transfusion-dependent beta
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The most common side effects observed in clinical studies included low levels of platelets and white blood cells, mouth sores, nausea, musculoskeletal pain, abdominal pain, vomiting, febrile neutropenia (fever and low white blood cell count), headache and itching.
878:"Vertex and CRISPR Therapeutics Announce Authorization of the First CRISPR/Cas9 Gene-Edited Therapy, Casgevy (exagamglogene autotemcel), by the United Kingdom MHRA for the Treatment of Sickle Cell Disease and Transfusion-Dependent Beta Thalassemia" 312:
The most common side effects include low levels of platelets and white blood cells, mouth sores, nausea, musculoskeletal pain, abdominal pain, vomiting, febrile neutropenia (fever and low white blood cell count), headache, and itching.
903: 796: 690: 1063: 753: 429:. The cost effectiveness threshold of the therapy in the US is estimated to be between $ 1.35 million and $ 2.05 million depending on perspective (healthcare vs limited societal) and assuming the 1031: 1546: 1000: 785: 1126: 682: 139: 1313: 790: 472: 468: 410: 1053: 63: 967: 741: 1090: 1058: 1095: 1023: 989: 1306: 340:
for the treatment of transfusion-dependent beta thalassemia and sickle cell disease in patients aged 12 years and older who should be treated with
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Text was copied from this source which is copyright European Medicines Agency. Reproduction is authorized provided the source is acknowledged.
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In the US, exagamglogene autotemcel is indicated for the treatment of sickle cell disease in people aged 12 years and older with recurrent
1118: 1299: 904:"Vertex and CRISPR Therapeutics Announce US FDA Approval of Casgevy (exagamglogene autotemcel) for the Treatment of Sickle Cell Disease" 629: 393: 114: 577: 509: 855: 534: 476: 169: 95: 396:, and regenerative medicine advanced therapy designations. The FDA granted approval of Casgevy to Vertex Pharmaceuticals. 1556: 961: 786:"MHRA authorises world-first gene therapy that aims to cure sickle-cell disease and transfusion-dependent β-thalassemia" 747: 571: 381: 325: 241: 1361: 1511: 1472: 434: 955: 930: 994: 623: 414: 1457: 1541: 1085: 125: 1239:"Efficacy and Safety of a Single Dose of Exagamglogene Autotemcel for Transfusion-Dependent β-Thalassemia" 655: 302: 1551: 1388: 348: 1161: 1439: 321: 306: 294: 1352: 1260: 1225: 1204:"Efficacy and Safety of a Single Dose of Exagamglogene Autotemcel for Severe Sickle Cell Disease" 1202:
Frangoul H, Locatelli F, Bhatia M, Mapara MY, Molinari L, Sharma A, et al. (November 2022).
1024:"In historic decision, FDA approves a CRISPR-based medicine for treatment of sickle cell disease" 847: 430: 1237:
Locatelli F, Lang P, Li A, Corbacioglu S, de la Fuente J, Wall DA, et al. (November 2022).
73: 1179: 839: 197: 184: 45: 1444: 1250: 1215: 1169: 831: 618: 298: 250: 1525: 385: 374: 33: 1165: 565: 501: 1535: 1462: 1413: 1372: 1367: 1264: 1229: 990:"First gene editing therapy to treat beta thalassemia and severe sickle cell disease" 851: 819: 772: 596: 87: 1448: 1408: 1403: 1394: 1357: 1347: 1333: 1323: 1291: 683:"FDA advisers see no roadblocks for gene-editing treatment for sickle cell disease" 290: 152: 147: 320:
Exagamglogene autotemcel is the first cell-based gene therapy treatment utilizing
1428: 1418: 1054:"ICER Publishes Final Evidence Report on Gene Therapies for Sickle Cell Disease" 389: 132: 81: 1174: 1149: 835: 351:, and for the treatment of people with transfusion-dependent beta-thalassemia. 1255: 1238: 1220: 1203: 742:"FDA Approves First Gene Therapies to Treat Patients with Sickle Cell Disease" 1482: 1477: 1423: 1342: 337: 67: 1183: 843: 1150:"UK first to approve CRISPR treatment for diseases: what you need to know" 221: 109: 1119:"Life-changing blood disease treatment approved at £1m cost per patient" 230: 1377: 17: 820:"The world's first CRISPR therapy is approved: who will receive it?" 270: 1498: 771:
This article incorporates text from this source, which is in the
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This article incorporates text from this source, which is in the
261: 203: 178: 1295: 191: 104: 880:(Press release). Vertex Pharmaceuticals. 16 November 2023. 384:(FDA) granted the application for exagamglogene autotemcel 906:(Press release). Vertex Pharmaceuticals. 8 December 2023. 344:
but for whom a suitable stem cell donor is not available.
535:"Casgevy- exagamglogene autotemcel injection, suspension" 502:"Casgevy 4–13 x 10Exp6 cells/mL dispersion for infusion" 1509: 1491: 1437: 1386: 1331: 791:
Medicines and Healthcare products Regulatory Agency
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Medicines and Healthcare products Regulatory Agency
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Archived from 1516: 453: 342:hematopoietic stem cell transplantation 336:In the UK, exagamglogene autotemcel is 229: 86: 31: 1129:from the original on 10 December 2023 1098:from the original on 14 November 2023 1003:from the original on 16 December 2023 884:from the original on 22 November 2023 799:from the original on 25 November 2023 632:from the original on 19 December 2023 580:from the original on 19 December 2023 72: 7: 1066:from the original on 4 December 2023 1034:from the original on 9 December 2023 970:from the original on 17 January 2024 910:from the original on 9 December 2023 858:from the original on 4 December 2023 756:from the original on 8 December 2023 693:from the original on 4 December 2023 660:Union Register of medicinal products 512:from the original on 9 December 2023 469:"Summary of Product Characteristics" 324:technology to be approved by the US 151: 999:(Press release). 15 December 2023. 795:(Press release). 16 November 2023. 425:The therapy has a US list price of 269: 966:(Press release). 16 January 2024. 25: 1519: 1022:Feuerstein A (8 December 2023). 766: 590: 440:The UK price is estimated to be 956:"FDA Roundup: January 16, 2024" 931:"FDA Roundup: January 16, 2024" 506:Electronic Medicines Compendium 437:(QALY) at $ 100,000–$ 150,000. 1: 656:"Casgevy product information" 317:thalassemia in January 2024. 1322:Other hematological agents ( 1086:"Value Assessment Framework" 962:Food and Drug Administration 818:Sheridan C (November 2023). 748:Food and Drug Administration 572:Food and Drug Administration 382:Food and Drug Administration 326:Food and Drug Administration 285:, sold under the brand name 1249:(Supplement 1): 4899–4901. 681:Stein R (31 October 2023). 1573: 1473:Lovotibeglogene autotemcel 1175:10.1038/d41586-023-03590-6 918:– via Business Wire. 892:– via Business Wire. 836:10.1038/d41587-023-00016-6 435:quality-adjusted life year 297:and transfusion-dependent 293:used for the treatment of 1256:10.1182/blood-2022-166881 1221:10.1182/blood-2022-162353 995:European Medicines Agency 624:European Medicines Agency 415:European Medicines Agency 1468:Exagamglogene autotemcel 1458:Betibeglogene autotemcel 1148:Wong C (November 2023). 322:CRISPR/Cas9 gene editing 283:Exagamglogene autotemcel 115:Exagamglogene autotemcel 34:Exagamglogene autotemcel 1214:(Supplement 1): 29–31. 409:In December 2023, the 303:Vertex Pharmaceuticals 301:. It was developed by 349:vaso-occlusive crises 824:Nature Biotechnology 628:. 14 December 2023. 508:. 24 November 2023. 1557:Sickle-cell disease 1440:sickle cell disease 1362:+desoxyribonuclease 1166:2023Natur.623..676W 752:. 8 December 2023. 576:. 8 December 2023. 400:Society and culture 307:CRISPR Therapeutics 295:sickle cell disease 187:(Prescription only) 36: 1353:Desoxyribonuclease 662:. 12 February 2024 482:on 8 December 2023 431:willingness to pay 1507: 1506: 1160:(7988): 676–677. 541:. 22 January 2024 280: 279: 207: 195: 182: 107: 16:(Redirected from 1564: 1524: 1523: 1522: 1515: 1445:beta thalassemia 1316: 1309: 1302: 1293: 1288: 1268: 1258: 1233: 1223: 1188: 1187: 1177: 1145: 1139: 1138: 1136: 1134: 1114: 1108: 1107: 1105: 1103: 1082: 1076: 1075: 1073: 1071: 1050: 1044: 1043: 1041: 1039: 1019: 1013: 1012: 1010: 1008: 986: 980: 979: 977: 975: 952: 946: 945: 943: 941: 926: 920: 919: 917: 915: 900: 894: 893: 891: 889: 874: 868: 867: 865: 863: 815: 809: 808: 806: 804: 782: 776: 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542: 533: 532: 525: 515: 513: 500: 499: 495: 485: 483: 479: 467: 466: 455: 450: 441: 427:US$ 2.2 million 426: 423: 407: 402: 386:priority review 375:graft rejection 370: 361: 334: 276: 256: 236: 211: 159: 127: 120: 58:CTX001, exa-cel 28: 23: 22: 15: 12: 11: 5: 1570: 1568: 1560: 1559: 1554: 1549: 1544: 1542:CRISPR therapy 1534: 1533: 1529: 1528: 1505: 1504: 1502: 1501: 1495: 1493: 1489: 1488: 1486: 1485: 1480: 1475: 1470: 1465: 1460: 1454: 1452: 1438:Drugs used in 1435: 1434: 1432: 1431: 1426: 1421: 1416: 1411: 1406: 1400: 1398: 1387:Drugs used in 1384: 1383: 1381: 1380: 1375: 1370: 1365: 1355: 1350: 1345: 1339: 1337: 1329: 1328: 1321: 1319: 1318: 1311: 1304: 1296: 1290: 1289: 1275: 1274:External links 1272: 1270: 1269: 1234: 1198: 1196: 1193: 1190: 1189: 1140: 1109: 1077: 1045: 1014: 981: 947: 921: 895: 869: 810: 777: 704: 673: 644: 619:"Casgevy EPAR" 601: 552: 523: 493: 452: 451: 449: 446: 422: 419: 413:(CHMP) of the 406: 403: 401: 398: 369: 366: 360: 357: 333: 330: 278: 277: 275: 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Retrieved 477:the original 439: 424: 408: 405:Legal status 379: 371: 362: 359:Side effects 353: 346: 335: 332:Medical uses 319: 315: 311: 291:gene therapy 286: 282: 281: 170:Legal status 164:Legal status 96:License data 29: 27:Gene therapy 1429:Lanadelumab 1419:Ecallantide 1133:10 December 1102:10 December 1038:10 December 1007:16 December 666:19 February 636:16 December 390:orphan drug 216:Identifiers 133:Intravenous 82:MedlinePlus 55:Other names 46:Trade names 1536:Categories 1391:angioedema 1389:hereditary 1070:4 December 974:17 January 940:19 January 914:9 December 888:9 December 862:4 December 830:(1): 3–4. 803:8 December 760:8 December 697:4 December 584:8 December 516:9 December 486:9 December 448:References 442:£1 million 394:fast track 251:S53L777GM8 1483:Voxelotor 1478:Mitapivat 1424:Icatibant 1343:Bromelain 1332:Enzymes ( 1265:256788715 1230:254352365 852:265350318 566:"Casgevy" 421:Economics 338:indicated 126:Routes of 74:Monograph 68:Drugs.com 1526:Medicine 1184:37974039 1127:Archived 1096:Archived 1064:Archived 1032:Archived 1001:Archived 968:Archived 908:Archived 882:Archived 856:Archived 844:37989785 797:Archived 754:Archived 691:Archived 630:Archived 578:Archived 539:DailyMed 510:Archived 222:DrugBank 140:ATC code 110:DailyMed 1378:Trypsin 1162:Bibcode 545:3 March 380:The US 368:History 328:(FDA). 289:, is a 287:Casgevy 231:DB15572 156:) 150: ( 148:B06AX05 112::  88:a624018 50:Casgevy 18:Exa-cel 1512:Portal 1492:Others 1263:  1228:  1182:  1154:Nature 850:  842:  793:(MHRA) 433:for 1 271:D12749 198:℞-only 196: 183: 108:  1499:Hemin 1449:B06AX 1395:B06AC 1334:B06AA 1261:S2CID 1243:Blood 1226:S2CID 1208:Blood 997:(EMA) 964:(FDA) 960:U.S. 848:S2CID 750:(FDA) 746:U.S. 626:(EMA) 574:(FDA) 570:U.S. 480:(PDF) 1443:and 1180:PMID 1135:2023 1104:2023 1072:2023 1040:2023 1028:STAT 1009:2023 976:2024 942:2024 916:2023 890:2023 864:2023 840:PMID 805:2023 762:2023 699:2023 668:2024 638:2023 586:2023 547:2024 518:2023 488:2023 305:and 262:KEGG 242:UNII 64:AHFS 1324:B06 1251:doi 1247:140 1216:doi 1212:140 1170:doi 1158:623 935:FDA 832:doi 687:NPR 185:POM 153:WHO 1538:: 1283:. 1259:. 1245:. 1241:. 1224:. 1210:. 1206:. 1178:. 1168:. 1156:. 1152:. 1125:. 1121:. 1094:. 1088:. 1062:. 1056:. 1030:. 1026:. 992:. 958:. 933:. 854:. 846:. 838:. 828:42 826:. 822:. 788:. 744:. 707:^ 689:. 685:. 658:. 647:^ 621:. 604:^ 568:. 555:^ 537:. 526:^ 504:. 471:. 456:^ 444:. 392:, 388:, 377:. 309:. 204:EU 192:US 179:UK 105:US 1514:: 1451:) 1447:( 1397:) 1393:( 1364:) 1360:( 1336:) 1326:) 1315:e 1308:t 1301:v 1287:. 1267:. 1253:: 1232:. 1218:: 1186:. 1172:: 1164:: 1137:. 1106:. 1074:. 1042:. 1011:. 978:. 944:. 866:. 834:: 807:. 775:. 764:. 701:. 670:. 640:. 599:. 588:. 549:. 520:. 490:. 206:: 194:: 181:: 66:/ 20:)

Index

Exa-cel
Trade names
AHFS
Drugs.com
Monograph
MedlinePlus
a624018
License data
DailyMed
Exagamglogene autotemcel
Routes of
administration

Intravenous
ATC code
B06AX05
WHO
Legal status
POM
℞-only
DrugBank
DB15572
UNII
S53L777GM8
KEGG
D12749
gene therapy
sickle cell disease
beta thalassemia
Vertex Pharmaceuticals
CRISPR Therapeutics
CRISPR/Cas9 gene editing

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