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Exagamglogene autotemcel

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406:(EMA) adopted a positive opinion, recommending the granting of a conditional marketing authorization for the medicinal product Casgevy, intended for the treatment of transfusion‑dependent β‑thalassemia and sickle cell disease. As Casgevy is an advanced therapy medicinal product, the CHMP positive opinion is based on an assessment by the Committee for Advanced Therapies. The applicant for this medicinal product is Vertex Pharmaceuticals (Ireland) Limited. Exagamglogene autotemcel was approved for medical use in the European Union in February 2024. 362:
prior to screening. The primary efficacy outcome was freedom from severe vaso-occlusive crisis episodes for at least twelve consecutive months during the 24-month follow-up period. A total of 44 participants were treated with exagamglogene autotemcel. Of the 31 participants with sufficient follow-up time to be evaluable, 29 (93.5%) achieved this outcome. All treated participants achieved successful engraftment with no participants experiencing graft failure or
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myeloablative conditioning (high-dose chemotherapy), a process that removes cells from the bone marrow so they can be replaced with the modified cells in exagamglogene autotemcel. The modified blood stem cells are transplanted back into the recipient where they engraft (attach and multiply) within the bone marrow and increase the production of fetal hemoglobin (HbF), a type of hemoglobin that facilitates oxygen delivery.
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The gene therapy is made from the recipient's own blood stem cells, which are modified, and are given back as a one-time, single-dose infusion as part of a hematopoietic (blood) stem cell transplant. Prior to treatment, the recipient's own stem cells are collected, and then the recipient must undergo
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The safety and effectiveness of exagamglogene autotemcel were evaluated in an ongoing single-arm, multi-center trial in adult and adolescent participants with sickle cell disease. Participants had a history of at least two protocol-defined severe vaso-occlusive crises during each of the two years
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The treatment was approved in the United Kingdom for the treatment of sickle cell disease and transfusion-dependent beta thalassemia in November 2023. It was approved in the United States for the treatment of sickle cell disease in December 2023 and for the treatment of transfusion-dependent beta
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The most common side effects observed in clinical studies included low levels of platelets and white blood cells, mouth sores, nausea, musculoskeletal pain, abdominal pain, vomiting, febrile neutropenia (fever and low white blood cell count), headache and itching.
867:"Vertex and CRISPR Therapeutics Announce Authorization of the First CRISPR/Cas9 Gene-Edited Therapy, Casgevy (exagamglogene autotemcel), by the United Kingdom MHRA for the Treatment of Sickle Cell Disease and Transfusion-Dependent Beta Thalassemia" 301:
The most common side effects include low levels of platelets and white blood cells, mouth sores, nausea, musculoskeletal pain, abdominal pain, vomiting, febrile neutropenia (fever and low white blood cell count), headache, and itching.
892: 785: 679: 1052: 742: 418:. The cost effectiveness threshold of the therapy in the US is estimated to be between $ 1.35 million and $ 2.05 million depending on perspective (healthcare vs limited societal) and assuming the 1020: 1535: 989: 774: 1115: 671: 128: 1302: 779: 461: 457: 399: 1042: 52: 956: 730: 1079: 1047: 1084: 1012: 978: 1295: 329:
for the treatment of transfusion-dependent beta thalassemia and sickle cell disease in patients aged 12 years and older who should be treated with
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Text was copied from this source which is copyright European Medicines Agency. Reproduction is authorized provided the source is acknowledged.
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In the US, exagamglogene autotemcel is indicated for the treatment of sickle cell disease in people aged 12 years and older with recurrent
1107: 1288: 893:"Vertex and CRISPR Therapeutics Announce US FDA Approval of Casgevy (exagamglogene autotemcel) for the Treatment of Sickle Cell Disease" 618: 382: 103: 566: 498: 844: 523: 465: 158: 84: 385:, and regenerative medicine advanced therapy designations. The FDA granted approval of Casgevy to Vertex Pharmaceuticals. 1545: 950: 775:"MHRA authorises world-first gene therapy that aims to cure sickle-cell disease and transfusion-dependent β-thalassemia" 736: 560: 370: 314: 230: 1350: 1500: 1461: 423: 944: 919: 983: 612: 403: 1446: 1530: 1074: 114: 1228:"Efficacy and Safety of a Single Dose of Exagamglogene Autotemcel for Transfusion-Dependent β-Thalassemia" 644: 291: 1540: 1377: 337: 1150: 1428: 310: 295: 283: 1341: 1249: 1214: 1193:"Efficacy and Safety of a Single Dose of Exagamglogene Autotemcel for Severe Sickle Cell Disease" 1191:
Frangoul H, Locatelli F, Bhatia M, Mapara MY, Molinari L, Sharma A, et al. (November 2022).
1013:"In historic decision, FDA approves a CRISPR-based medicine for treatment of sickle cell disease" 836: 419: 1226:
Locatelli F, Lang P, Li A, Corbacioglu S, de la Fuente J, Wall DA, et al. (November 2022).
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Exagamglogene autotemcel is the first cell-based gene therapy treatment utilizing
1417: 1407: 1043:"ICER Publishes Final Evidence Report on Gene Therapies for Sickle Cell Disease" 378: 121: 70: 1163: 1138: 824: 340:, and for the treatment of people with transfusion-dependent beta-thalassemia. 1244: 1227: 1209: 1192: 731:"FDA Approves First Gene Therapies to Treat Patients with Sickle Cell Disease" 1471: 1466: 1412: 1331: 326: 56: 1172: 832: 1139:"UK first to approve CRISPR treatment for diseases: what you need to know" 210: 98: 1108:"Life-changing blood disease treatment approved at £1m cost per patient" 219: 1366: 809:"The world's first CRISPR therapy is approved: who will receive it?" 259: 1487: 760:
This article incorporates text from this source, which is in the
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This article incorporates text from this source, which is in the
250: 192: 167: 1284: 180: 93: 869:(Press release). Vertex Pharmaceuticals. 16 November 2023. 373:(FDA) granted the application for exagamglogene autotemcel 895:(Press release). Vertex Pharmaceuticals. 8 December 2023. 333:
but for whom a suitable stem cell donor is not available.
524:"Casgevy- exagamglogene autotemcel injection, suspension" 491:"Casgevy 4–13 x 10Exp6 cells/mL dispersion for infusion" 1498: 1480: 1426: 1375: 1320: 780:
Medicines and Healthcare products Regulatory Agency
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Medicines and Healthcare products Regulatory Agency
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Archived from 1505: 442: 331:hematopoietic stem cell transplantation 325:In the UK, exagamglogene autotemcel is 218: 75: 20: 1118:from the original on 10 December 2023 1087:from the original on 14 November 2023 992:from the original on 16 December 2023 873:from the original on 22 November 2023 788:from the original on 25 November 2023 621:from the original on 19 December 2023 569:from the original on 19 December 2023 61: 7: 1055:from the original on 4 December 2023 1023:from the original on 9 December 2023 959:from the original on 17 January 2024 899:from the original on 9 December 2023 847:from the original on 4 December 2023 745:from the original on 8 December 2023 682:from the original on 4 December 2023 649:Union Register of medicinal products 501:from the original on 9 December 2023 458:"Summary of Product Characteristics" 313:technology to be approved by the US 140: 988:(Press release). 15 December 2023. 784:(Press release). 16 November 2023. 414:The therapy has a US list price of 258: 955:(Press release). 16 January 2024. 14: 1508: 1011:Feuerstein A (8 December 2023). 755: 579: 429:The UK price is estimated to be 945:"FDA Roundup: January 16, 2024" 920:"FDA Roundup: January 16, 2024" 495:Electronic Medicines Compendium 426:(QALY) at $ 100,000–$ 150,000. 1: 645:"Casgevy product information" 306:thalassemia in January 2024. 1311:Other hematological agents ( 1075:"Value Assessment Framework" 951:Food and Drug Administration 807:Sheridan C (November 2023). 737:Food and Drug Administration 561:Food and Drug Administration 371:Food and Drug Administration 315:Food and Drug Administration 274:, sold under the brand name 1238:(Supplement 1): 4899–4901. 670:Stein R (31 October 2023). 1562: 1462:Lovotibeglogene autotemcel 1164:10.1038/d41586-023-03590-6 907:– via Business Wire. 881:– via Business Wire. 825:10.1038/d41587-023-00016-6 424:quality-adjusted life year 286:and transfusion-dependent 282:used for the treatment of 1245:10.1182/blood-2022-166881 1210:10.1182/blood-2022-162353 984:European Medicines Agency 613:European Medicines Agency 404:European Medicines Agency 1457:Exagamglogene autotemcel 1447:Betibeglogene autotemcel 1137:Wong C (November 2023). 311:CRISPR/Cas9 gene editing 272:Exagamglogene autotemcel 104:Exagamglogene autotemcel 23:Exagamglogene autotemcel 1203:(Supplement 1): 29–31. 398:In December 2023, the 292:Vertex Pharmaceuticals 290:. It was developed by 338:vaso-occlusive crises 813:Nature Biotechnology 617:. 14 December 2023. 497:. 24 November 2023. 1546:Sickle-cell disease 1429:sickle cell disease 1351:+desoxyribonuclease 1155:2023Natur.623..676W 741:. 8 December 2023. 565:. 8 December 2023. 389:Society and culture 296:CRISPR Therapeutics 284:sickle cell disease 176:(Prescription only) 25: 1342:Desoxyribonuclease 651:. 12 February 2024 471:on 8 December 2023 420:willingness to pay 1496: 1495: 1149:(7988): 676–677. 530:. 22 January 2024 269: 268: 196: 184: 171: 96: 1553: 1513: 1512: 1511: 1504: 1434:beta thalassemia 1305: 1298: 1291: 1282: 1277: 1257: 1247: 1222: 1212: 1177: 1176: 1166: 1134: 1128: 1127: 1125: 1123: 1103: 1097: 1096: 1094: 1092: 1071: 1065: 1064: 1062: 1060: 1039: 1033: 1032: 1030: 1028: 1008: 1002: 1001: 999: 997: 975: 969: 968: 966: 964: 941: 935: 934: 932: 930: 915: 909: 908: 906: 904: 889: 883: 882: 880: 878: 863: 857: 856: 854: 852: 804: 798: 797: 795: 793: 771: 765: 759: 758: 754: 752: 750: 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488: 484: 474: 472: 468: 456: 455: 444: 439: 430: 416:US$ 2.2 million 415: 412: 396: 391: 375:priority review 364:graft rejection 359: 350: 323: 265: 245: 225: 200: 148: 116: 109: 47:CTX001, exa-cel 17: 12: 11: 5: 1559: 1557: 1549: 1548: 1543: 1538: 1533: 1531:CRISPR therapy 1523: 1522: 1518: 1517: 1494: 1493: 1491: 1490: 1484: 1482: 1478: 1477: 1475: 1474: 1469: 1464: 1459: 1454: 1449: 1443: 1441: 1427:Drugs used in 1424: 1423: 1421: 1420: 1415: 1410: 1405: 1400: 1395: 1389: 1387: 1376:Drugs used in 1373: 1372: 1370: 1369: 1364: 1359: 1354: 1344: 1339: 1334: 1328: 1326: 1318: 1317: 1310: 1308: 1307: 1300: 1293: 1285: 1279: 1278: 1264: 1263:External links 1261: 1259: 1258: 1223: 1187: 1185: 1182: 1179: 1178: 1129: 1098: 1066: 1034: 1003: 970: 936: 910: 884: 858: 799: 766: 693: 662: 633: 608:"Casgevy EPAR" 590: 541: 512: 482: 441: 440: 438: 435: 411: 408: 402:(CHMP) of the 395: 392: 390: 387: 358: 355: 349: 346: 322: 319: 267: 266: 264: 263: 255: 253: 247: 246: 244: 243: 235: 233: 227: 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Index

Trade names
AHFS
Drugs.com
Monograph
MedlinePlus
a624018
License data
DailyMed
Exagamglogene autotemcel
Routes of
administration

Intravenous
ATC code
B06AX05
WHO
Legal status
POM
℞-only
DrugBank
DB15572
UNII
S53L777GM8
KEGG
D12749
gene therapy
sickle cell disease
beta thalassemia
Vertex Pharmaceuticals
CRISPR Therapeutics
CRISPR/Cas9 gene editing
Food and Drug Administration

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