40:
653:
224:
1706:
571:
1332:
1309:
1294:
1410:
1099:
Schreuder, Michiel F. (2015). "Renal hypoplasia". In Turner, Neil N.; Turner, Neil N.; Lameire, Norbert; Goldsmith, David J.; Winearls, Christopher G.; Himmelfarb, Jonathan; Remuzzi, Giuseppe (eds.).
1403:
463:
from the average, with the weight often being over 50g in adults and 12â25g in children. This type of hypoplasia can be either unilateral or bilateral and is more prevalent in
606:
We find the etiology of this condition is in the mutations in kidney-related genes, namely, HNF1B, PAX2, PBX1. However, environmental factors like maternal diseases such as
1396:
550:
to decrease in thickness throughout the person's life. This type of hypoplasia is frequently paired with other forms of renal hypoplasia and seems to portray an arrest of
1736:
1165:
1052:"Renal Hypoplasia, From Grossly Insufficient to Not Quite Enough: Consideration for Expanded Concepts Based Upon the Author's Perspective With Historical Review"
942:"Renal Hypoplasia, From Grossly Insufficient to Not Quite Enough: Consideration for Expanded Concepts Based Upon the Author's Perspective With Historical Review"
518:
are absent. The surface of the kidney has a pelvic recess and one or more transverse cortical grooves, presumed to be a failed formation of a renal lobe. The
554:, leading to fewer nephron generations, resulting in smaller renal size in general. The nephrogenesis before the arrest is normal. On the other hand, the
1179:
251:
weighing 50% or less of that of the normal, or the combined weight of both kidneys being less than 33% of that of the normal. Often accompanied by
283:
are absent and apart from its decreased size, every other facet of the kidneys is unaffected. If unilateral, the contralateral kidney can undergo
1116:
854:
239:. The classification of renal hypoplasia establishes four types, termed simple, oligomeganephronic, segmental, and cortical.
1731:
1488:
331:
359:
327:
582:
number, but normal corticomedullary differentiation. The condition is usually asymptomatic, otherwise infection and
354:
is reduced to five to six or occasionally as few as one or two. The number of nephrons per lobe is reduced as well.
1696:
440:
435:
411:
367:
347:
112:
77:
39:
1624:
1478:
661:
660:
In terms of the treatment of renal hypoplasia, we find it depends on the severity of the chronic kidney disease.
97:
1619:
1388:
1679:
1583:
1493:
555:
503:
423:
355:
93:
64:
1376:
1140:
768:
288:
177:
151:
73:
1472:
1464:
499:
363:
323:
268:
1644:
1517:
1303:
626:
In terms of the diagnosis of renal hypoplasia, we find that the following is done in its evaluation:
343:
193:
101:
1726:
1419:
1336:
487:
346:
is normal. The combined length of both kidneys is 80% or lower than a single normal kidney and the
287:
to compensate for the affected kidney, and renal function stays normal. If bilateral, progressive
615:
551:
460:
200:
837:
Copelovitch, Lawrence; Kaplan, Bernard S. (2012). "Developmental
Abnormalities of the Kidneys".
1591:
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1081:
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981:
963:
904:
850:
819:
139:
52:
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1071:
1063:
1022:
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971:
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894:
842:
809:
799:
519:
387:
383:
788:"Unilateral hypoplastic kidney in adults: An experience of a tertiary-level urology center"
1710:
1674:
1534:
1483:
1459:
883:"Genetics of Renal Hypoplasia: Insights Into the Mechanisms Controlling Nephron Endowment"
379:
256:
156:
1108:
881:
Cain, Jason E; Di
Giovanni, Valeria; Smeeton, Joanna; Rosenblum, Norman D (August 2010).
522:
next to the hypoplastic part of the kidney is seemingly normal; however, it can undergo
1552:
1449:
1441:
1426:
1076:
1051:
1027:
1000:
976:
941:
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814:
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559:
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419:
339:
303:
1341:
1720:
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1507:
731:
708:
543:
495:
375:
311:
1669:
652:
611:
583:
547:
491:
479:
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with the same condition. In the first few years of the affected individual's life,
371:
263:
is reduced to five or fewer, compared to the usual ten or more. Enlargement of the
252:
81:
562:
have decreased in size with the radial glomerular count reduced to eight or less.
1067:
958:
899:
882:
1614:
523:
515:
483:
415:
399:
284:
260:
85:
207:, and the morphology is normal. The severity of the disease depends on whether
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685:
535:
507:
456:
452:
407:
351:
315:
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185:
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57:
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1347:
723:
511:
475:
280:
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1230:
1085:
1036:
985:
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823:
199:
It is defined as abnormally small kidneys, where the size is less than two
1286:
804:
672:
Epidemiologic studies point to an estimated incidence of 1 in 400 births.
1371:
641:
607:
403:
211:
is unilateral or bilateral, and the degree of reduction in the number of
1205:
1661:
1601:
636:
579:
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307:
264:
223:
212:
189:
1544:
1313:
1298:
468:
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448:
335:
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181:
89:
69:
570:
422:
to come after, its onset determined by the combined renal mass. The
693:
651:
569:
471:
222:
124:
47:
An ultrasound scan of a hypoplastic right kidney in an adult male.
1352:
786:
Gadelkareem, Rabea Ahmed; Mohammed, Nasreldin (25 January 2022).
391:
374:
is rarely present in this type. The affected are generally born
319:
299:
Oligomeganephronia (or oligomeganephronic hypoplasia) is a rare
132:
128:
1392:
267:
is not present in this type, considering it is associated with
1206:"renal | Etymology, origin and meaning of renal by etymonline"
235:
Renal hypoplasia pertains to the reduction in the number of
1001:"A Case Report and Literature Review of Oligomeganephronia"
390:. It has been reported that the affected person can have a
534:
Cortical hypoplasia is a not widely known type of renal
1694:
322:
with a ratio of three-to-one and is caused by either
1276:
1660:
1653:
1637:
1600:
1582:
1575:
1543:
1440:
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1362:
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999:Wang, XH; Pan, L; He, S; Kong, DL; Wang, W (2022).
163:
150:
138:
119:
107:
63:
51:
29:
24:
459:is reduced, and the kidney size is less than two
247:Simple hypoplasia is characterized by either one
426:occurs between six months and seventeen years.
350:is reduced to 30% of the normal. The number of
338:are affected symmetrically unless paired with
203:below the expected mean for the corresponding
1404:
1256:"plasia | Search Online Etymology Dictionary"
598:in children and also of adult-onset disease.
8:
1231:"hypo | Search Online Etymology Dictionary"
1164:: CS1 maint: numeric names: authors list (
927:Principles of Renal Physiology, 5th edition
1657:
1579:
1437:
1411:
1397:
1389:
1277:
1184:Centers for Disease Control and Prevention
498:is either non-existent or underdeveloped.
38:
21:
1075:
1026:
1016:
975:
957:
898:
813:
803:
1701:
769:"S. Kohl, M. Liebau - Renal hypoplasia"
747:
310:is reduced but is distinctly enlarged.
1737:Congenital disorders of urinary system
1157:
1134:
1132:
1130:
1128:
1101:Oxford Textbook of Clinical Nephrology
920:
918:
876:
874:
872:
870:
868:
866:
763:
761:
759:
757:
755:
753:
751:
594:Renal hypoplasia is a common cause of
526:, making the grooves more noticeable.
1050:Bonsib, Stephen M. (September 2020).
940:Bonsib, Stephen M. (September 2020).
692:(ârelated to the kidneysâ), from the
16:Congenital abnormality of the kidneys
7:
1139:RESERVED, INSERM US14-- ALL RIGHTS.
542:generations is reduced, causing the
614:, and intoxication via smoking and
578:Hypoplastic kidneys have a reduced
1109:10.1093/med/9780199592548.003.0348
847:10.1016/B978-1-4377-0134-0.10083-6
14:
1704:
618:are linked to renal hypoplasia.
314:are also enlarged. This type of
839:Avery's Diseases of the Newborn
443:or Ask-Upmark kidney is a rare
1423:malformations and deformations
1056:Advances in Anatomic Pathology
946:Advances in Anatomic Pathology
1:
1489:Multicystic dysplastic kidney
925:Lote, Christopher J. (2012).
1141:"Orphanet: Renal hypoplasia"
1068:10.1097/PAP.0000000000000269
959:10.1097/PAP.0000000000000269
900:10.1203/PDR.0b013e3181e35a88
506:are commonly present, while
180:in which one or both of the
111:Simple, oligomeganephronic,
1180:"Renal Agenesis/Hypoplasia"
792:World Journal of Nephrology
1753:
546:to reduce in size and the
436:Renal segmental hypoplasia
433:
348:glomerular filtration rate
330:, acro renal syndrome, or
78:glomerular hyperfiltration
1625:Penoscrotal transposition
1620:Posterior urethral valves
1479:Polycystic kidney disease
662:Renal replacement therapy
410:are present, followed by
366:is insignificant. Unlike
358:of the urinary tract and
328:branchiootorenal syndrome
231:with renal pyramid below)
227:Renal lobe (renal cortex
188:, resulting in a reduced
98:urinary tract obstruction
46:
37:
1018:10.3389/fmed.2022.811992
738:(âmolding, formationâ).
504:urinary tract infections
332:wolf-hirschhorn syndrome
1494:Medullary sponge kidney
929:. Springer. p. 22.
424:end-stage renal disease
324:renal-coloboma syndrome
192:number but with normal
94:urinary tract infection
841:. pp. 1182â1190.
657:
575:
232:
178:congenital abnormality
152:Differential diagnosis
123:Mutation of the genes
74:chronic kidney disease
1465:Papillorenal syndrome
1005:Frontiers in Medicine
805:10.5527/wjn.v11.i1.30
655:
586:formation can occur.
573:
500:Vesicoureteral reflux
482:and is often severe.
364:vesicoureteral reflux
342:, which is uncommon.
318:is more prevalent in
226:
1732:Congenital disorders
1645:Prune belly syndrome
1518:Supernumerary kidney
633:Abdominal ultrasound
538:where the number of
447:where a part of the
441:Segmental hypoplasia
430:Segmental hypoplasia
368:segmental hypoplasia
306:where the number of
159:, oligomeganephronia
530:Cortical hypoplasia
461:standard deviations
418:, with progressive
378:or small for their
340:unilateral agenesis
289:renal insufficiency
201:standard deviations
186:smaller than normal
33:Hypoplastic kidneys
1363:External resources
1260:www.etymonline.com
1235:www.etymonline.com
1210:www.etymonline.com
887:Pediatric Research
664:is a possibility.
658:
576:
566:Signs and symptoms
490:are absent in the
295:Oligomeganephronia
269:oligomeganephronia
233:
1692:
1691:
1688:
1687:
1633:
1632:
1592:Bladder exstrophy
1571:
1570:
1563:Duplicated ureter
1386:
1385:
1118:978-0-19-959254-8
856:978-1-4377-0134-0
382:. Most cases are
243:Simple hypoplasia
171:
170:
140:Diagnostic method
19:Medical condition
1744:
1709:
1708:
1707:
1700:
1658:
1580:
1513:Nephronophthisis
1503:Horseshoe kidney
1455:Renal hypoplasia
1438:
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1136:
1123:
1122:
1103:. p. 2832.
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996:
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989:
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878:
861:
860:
834:
828:
827:
817:
807:
783:
777:
776:
765:
520:renal parenchyma
455:. The number of
255:. The number of
174:Renal hypoplasia
42:
25:Renal hypoplasia
22:
1752:
1751:
1747:
1746:
1745:
1743:
1742:
1741:
1717:
1716:
1715:
1705:
1703:
1695:
1693:
1684:
1675:Urachal fistula
1649:
1629:
1596:
1567:
1539:
1535:Alport syndrome
1484:Meckel syndrome
1460:Potter sequence
1429:
1417:
1387:
1382:
1381:
1358:
1357:
1289:
1275:
1274:
1264:
1262:
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1199:
1189:
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1186:. 17 March 2021
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916:
880:
879:
864:
857:
836:
835:
831:
785:
784:
780:
767:
766:
749:
744:
722:comes from the
707:comes from the
684:comes from the
678:
670:
650:
624:
604:
592:
568:
532:
438:
432:
412:hyperfiltration
380:gestational age
362:are absent and
360:nephrosclerosis
297:
245:
221:
167:1 in 400 births
157:Renal dysplasia
20:
17:
12:
11:
5:
1750:
1748:
1740:
1739:
1734:
1729:
1719:
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1606:
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1598:
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1588:
1586:
1577:
1573:
1572:
1569:
1568:
1566:
1565:
1560:
1555:
1553:Ectopic ureter
1549:
1547:
1541:
1540:
1538:
1537:
1532:
1530:Dent's disease
1526:
1525:
1520:
1515:
1510:
1505:
1499:
1498:
1497:
1496:
1491:
1486:
1481:
1468:
1467:
1462:
1457:
1452:
1450:Renal agenesis
1446:
1444:
1435:
1431:
1430:
1427:urinary system
1418:
1416:
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1408:
1401:
1393:
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1364:
1360:
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1356:
1355:
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1290:
1285:
1284:
1282:
1281:Classification
1273:
1272:
1247:
1222:
1197:
1171:
1124:
1117:
1091:
1062:(5): 311â330.
1042:
991:
952:(5): 311â330.
932:
914:
862:
855:
829:
778:
746:
745:
743:
740:
677:
674:
669:
666:
649:
646:
645:
644:
639:
634:
631:
623:
620:
603:
600:
596:kidney failure
591:
588:
567:
564:
560:renal pyramids
556:medullary rays
531:
528:
486:are enlarged,
451:has undergone
434:Main article:
431:
428:
296:
293:
244:
241:
220:
219:Classification
217:
169:
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148:
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117:
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109:
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67:
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55:
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35:
34:
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27:
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18:
15:
13:
10:
9:
6:
4:
3:
2:
1749:
1738:
1735:
1733:
1730:
1728:
1725:
1724:
1722:
1712:
1702:
1698:
1681:
1680:Urachal sinus
1678:
1676:
1673:
1671:
1668:
1667:
1665:
1663:
1659:
1656:
1652:
1646:
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1550:
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1542:
1536:
1533:
1531:
1528:
1527:
1524:
1523:Pelvic kidney
1521:
1519:
1516:
1514:
1511:
1509:
1508:Renal ectopia
1506:
1504:
1501:
1500:
1495:
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1211:
1207:
1201:
1198:
1185:
1181:
1175:
1172:
1167:
1161:
1146:
1145:www.orpha.net
1142:
1135:
1133:
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1125:
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1114:
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830:
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774:
773:www.orpha.net
770:
764:
762:
760:
758:
756:
754:
752:
748:
741:
739:
737:
733:
732:Ancient Greek
729:
725:
721:
716:
714:
710:
709:Ancient Greek
706:
701:
700:(âkidneysâ).
699:
695:
691:
687:
683:
675:
673:
667:
665:
663:
654:
647:
643:
640:
638:
635:
632:
630:Clinical exam
629:
628:
627:
621:
619:
617:
613:
609:
601:
599:
597:
590:Complications
589:
587:
585:
581:
572:
565:
563:
561:
557:
553:
552:nephrogenesis
549:
545:
544:renal medulla
541:
537:
529:
527:
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521:
517:
513:
509:
505:
501:
497:
493:
489:
485:
481:
477:
473:
470:
466:
462:
458:
454:
450:
446:
445:renal disease
442:
437:
429:
427:
425:
421:
420:renal failure
417:
413:
409:
405:
401:
397:
393:
389:
386:but some are
385:
381:
377:
373:
369:
365:
361:
357:
356:Malformations
353:
349:
345:
341:
337:
333:
329:
325:
321:
317:
313:
309:
305:
304:renal disease
302:
294:
292:
291:is expected.
290:
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65:Complications
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1670:Urachal cyst
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893:(2): 91â98.
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798:(1): 30â38.
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735:
734:word ĎΝΏĎΚĎ
727:
719:
717:
712:
704:
702:
697:
689:
681:
679:
671:
668:Epidemiology
659:
656:Hemodialysis
625:
612:hypertension
605:
593:
584:kidney stone
577:
574:Kidney stone
548:renal cortex
533:
480:hypertension
467:by 72%. The
439:
372:hypertension
298:
253:hypertension
246:
234:
228:
205:demographics
198:
173:
172:
102:urolithiasis
82:hypertension
1615:Hypospadias
730:, from the
718:The suffix
715:(âunderâ).
703:The prefix
524:hypertrophy
516:proteinuria
457:renal lobes
416:proteinuria
400:dehydration
352:renal lobes
285:hypertrophy
275:is normal.
237:renal lobes
86:proteinuria
30:Other names
1727:Nephrology
1721:Categories
1610:Epispadias
1558:Megaureter
1420:Congenital
1011:: 811992.
742:References
686:Late Latin
648:Management
536:hypoplasia
494:, and the
478:, causing
474:is overly
453:hypoplasia
414:alongside
408:polydipsia
344:Morphology
316:hypoplasia
209:hypoplasia
194:morphology
145:Ultrasound
115:, cortical
58:Nephrology
1654:Vestigial
1434:Abdominal
1348:SNOMED CT
1265:26 August
1240:26 August
1215:26 August
1190:16 August
1150:16 August
968:1533-4031
724:Neo-Latin
711:word á˝ĎÎż
680:The word
676:Etymology
622:Diagnosis
512:dysplasia
488:glomeruli
388:inherited
376:premature
301:pediatric
281:dysplasia
273:histology
164:Frequency
113:segmental
53:Specialty
1711:Medicine
1372:Orphanet
1353:32659003
1160:cite web
1086:32520748
1037:35391889
986:32520748
909:20421843
824:35117977
642:MRI scan
608:diabetes
476:secreted
404:polyuria
384:sporadic
308:nephrons
265:nephrons
213:nephrons
1662:Urachus
1602:Urethra
1584:Bladder
1304:LB30.0Y
1077:7458098
1028:8980273
977:7458098
815:8790306
720:-plasia
690:renalis
637:CT scan
616:alcohol
580:nephron
540:nephron
496:medulla
484:Calyces
465:females
396:sibling
336:kidneys
334:. Both
312:Tubules
261:calyces
257:lobules
190:nephron
182:kidneys
1697:Portal
1576:Pelvic
1545:Ureter
1473:cystic
1442:Kidney
1115:
1084:
1074:
1035:
1025:
984:
974:
966:
907:
853:
822:
812:
736:plĂĄsis
728:plasia
602:Causes
514:, and
492:cortex
469:enzyme
449:kidney
271:. The
249:kidney
120:Causes
90:sepsis
70:Anuria
1377:93101
1342:753.0
1327:Q60.5
1323:Q60.4
1319:Q60.3
726:word
705:hypo-
698:renes
696:word
694:Latin
688:word
682:renal
508:cysts
472:renin
320:males
277:Cysts
229:green
176:is a
125:HNF1B
108:Types
1638:Both
1337:9-CM
1267:2023
1242:2023
1217:2023
1192:2023
1166:link
1152:2023
1113:ISBN
1082:PMID
1033:PMID
982:PMID
964:ISSN
905:PMID
851:ISBN
820:PMID
713:hupo
558:and
502:and
406:and
392:twin
259:and
184:are
133:PBX1
129:PAX2
1425:of
1333:ICD
1310:ICD
1295:ICD
1105:doi
1072:PMC
1064:doi
1023:PMC
1013:doi
972:PMC
954:doi
895:doi
843:doi
810:PMC
800:doi
394:or
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