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IVEMARK, BI. (November 1955). "Implications of agenesis of the spleen on the pathogenesis of conotruncus anomalies in childhood; an analysis of the heart malformations in the splenic agenesis syndrome, with fourteen new cases".
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In right atrial isomerism, both atria of the heart are morphological right atria leading to associated abnormalities in the pulmonary venous system. In addition, individuals with right atrial isomerism develop
259:
Konstantinidou, A.; Sifakis, S.; Koukoura, O.; Mantas, N.; Agrogiannis, G.; Patsouris, E. (Aug 2008). "Pancreatic aplasia in a fetus with asplenia-cardiovascular defect-heterotaxy (Ivemark syndrome)".
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109:, a midline liver, malrotation of the small intestine and the presence of two morphologic right lungs. Individuals with left atrial isomerism, by comparison, have two morphologic left atria,
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are characterized by defects in the heart, spleen and paired organs such as the lungs and kidneys. Another name is "asplenia-cardiovascular defect-heterotaxy".
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Right atrial isomerism is named for its discoverer, Swedish pathologist
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Birth
Defects Research Part A: Clinical and Molecular Teratology
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This condition is inherited in an autosomal recessive manner
113:, intestinal malrotation and two morphologic left lungs.
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368:"'Jigsaw Kid' lives with jumbled up internal organs"
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343:National Organization for Rare Diseases
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587:Asplenia with cardiovascular anomalies
71:Asplenia with cardiovascular anomalies
22:Asplenia with cardiovascular anomalies
659:Intranodal palisaded myofibroblastoma
7:
121:The cause of heterotaxy is unknown.
309:10.1111/j.1651-2227.1955.tb05346.x
14:
762:Postmastectomy lymphangiosarcoma
730:Lymphedema–distichiasis syndrome
378:from the original on 25 May 2009
349:from the original on 28 May 2009
241:from the original on 30 May 2009
182:
143:
675:Template:Respiratory pathology
231:"Ivemark Syndrome Association"
1:
126:Ivemark Syndrome Association
757:Postinflammatory lymphedema
649:Generalized lymphadenopathy
517:: organ and vessel diseases
297:Acta Paediatrica Supplement
811:
43:
34:
191:This section is empty.
152:This section is empty.
79:right atrial isomerism
715:Congenital lymphedema
81:, is an example of a
795:Congenital disorders
752:Factitial lymphedema
742:Secondary lymphedema
303:(Suppl 104): 7–110.
128:, which is based in
87:congenital disorders
654:Castleman's disease
83:heterotaxy syndrome
747:Bullous lymphedema
720:Lymphedema praecox
710:Primary lymphedema
621:Splenic infarction
458:External resources
339:"Ivemark Syndrome"
273:10.1002/bdra.20467
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687:Lymphatic vessels
547:DiGeorge syndrome
515:Lymphatic disease
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85:. These uncommon
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16:Medical condition
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769:Waldmann disease
735:Milroy's disease
725:Lymphedema tarda
700:Lymphangiectasia
614:Banti's syndrome
604:Wandering spleen
594:Accessory spleen
564:Thymic carcinoma
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75:Ivemark syndrome
73:, also known as
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55:Medical genetics
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30:Ivemark syndrome
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644:Lymphadenopathy
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402:Classification
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374:. 2009-05-22.
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695:Lymphangitis
609:Splenomegaly
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380:. Retrieved
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351:. Retrieved
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267:(8): 601–4.
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100:Presentation
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599:Polysplenia
537:Hyperplasia
111:polysplenia
27:Other names
784:Categories
705:Lymphedema
636:Lymph node
542:Hypoplasia
382:2009-05-24
353:2009-05-24
245:2009-05-27
235:Patient UK
214:References
325:221418617
202:July 2017
175:Treatment
163:July 2017
136:Diagnosis
50:Specialty
582:Asplenia
467:Orphanet
376:Archived
347:Archived
317:13292296
281:18496831
239:Archived
107:asplenia
669:Tonsils
559:Thymoma
532:Abscess
423:: Q20.6
574:Spleen
524:Thymus
448:208530
323:
315:
279:
130:Dorset
117:Causes
57:
472:97548
437:759.0
321:S2CID
673:see
443:OMIM
432:9-CM
313:PMID
277:PMID
124:The
77:and
428:ICD
416:ICD
305:doi
269:doi
197:.
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408:D
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Text is available under the Creative Commons Attribution-ShareAlike License. Additional terms may apply.
