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The tumor is rare. It accounts for around 12% of cases of Ewing sarcoma. It is 10 times less common than Ewing sarcoma of bone and occurs in around 1.4 per million people, with a greater likelihood in under five-year olds and over 35-year olds. There does not appear to be any association with
129:. Typical symptoms include pain at the site of the tumor. It can occur in a wide range of parts of the body. It grows rapidly, with the upper leg, upper arms, bottom and shoulders being the most common sites to be affected. At presentation, a quarter of cases have already
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WHO Classification of
Tumours Editorial Board, ed. (2020). "2. Undifferentiated small round cell sarcoma of bone and soft tissue: Ewing sarcoma".
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Veselis, Clinton A.; Awan, Omer; Thomas, Ashanth; Ling, Stephen; Jonnalagadda, Padmaja; Aneja, Amandeep; Ali, Sayed (May 2021).
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348:"Bone Tumors Occurring in the Soft Tissues: A Review of the Clinical, Imaging, and Histopathologic Findings"
232:. Vol. 3 (5th ed.). Lyon (France): International Agency for Research on Cancer. pp. 323–325.
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Chemotherapy and surgical removal are options if the tumor is localised. If it cannot be operated upon,
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Abboud, A; Masrouha, K; Saliba, M; Haidar, R; Saab, R; Khoury, N; Tawil, A; Saghieh, S (May 2021).
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in detecting spread, and can be used to monitor response to treatment.
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299:"Extraskeletal Ewing sarcoma: Diagnosis, management and prognosis"
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Soft Tissue and Bone
Tumours: WHO Classification of Tumours
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153:, and confirmed by CT-guided or ultrasound-guided
416:Tefft, M.; Vawter, G. F.; Mitus, A. (June 1969).
92:Chemotherapy, surgical removal, radiation therapy
418:"Paravertebral "round cell" tumors in children"
163:Fluorodeoxyglucose-positron emission tomography
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352:Current Problems in Diagnostic Radiology
72:Rapid, <5years and >35years of age
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198:The condition was first reported by
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117:that does not arise from bone.
394:from the original on 2021-03-30
246:from the original on 2021-06-13
364:10.1067/j.cpradiol.2020.06.004
161:has excluded spread to lungs.
100:0.4 per million, males=females
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52:Pain at the site of the tumor
107:Extraskeletal Ewing sarcoma
22:Extraskeletal Ewing sarcoma
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113:of soft tissue, a type of
30:Extraosseous Ewing sarcoma
149:being more accurate than
165:is more accurate than a
127:Ewing family of tumors
315:10.3892/ol.2021.12615
190:ethnicity or gender.
181:may be effective.
558:External resources
155:core-needle biopsy
125:It belongs to the
121:Signs and symptoms
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239:978-92-832-4503-2
179:radiation therapy
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200:Melvin Tefft
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185:Epidemiology
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109:(EES), is a
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567:MedlinePlus
69:Usual onset
27:Other names
599:Categories
543:DiseasesDB
398:2022-06-20
309:(5): 354.
250:2021-05-09
206:References
578:eMedicine
442:0033-8419
422:Radiology
388:220530415
372:1535-6302
202:in 1969.
173:Treatment
167:bone scan
137:Diagnosis
97:Frequency
89:Treatment
36:Specialty
583:ped/2589
392:Archived
380:32665061
333:33747211
244:Archived
159:chest CT
48:Symptoms
41:Oncology
610:Sarcoma
537:D012512
515:M9260/3
450:5799839
324:7967932
194:History
157:once a
151:CT scan
145:, with
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111:cancer
63:Spread
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489:C41.9
384:S2CID
548:4604
532:MeSH
521:OMIM
499:9-CM
446:PMID
438:ISSN
376:PMID
368:ISSN
329:PMID
234:ISBN
495:ICD
480:ICD
430:doi
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319:PMC
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147:MRI
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