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Foix–Alajouanine syndrome

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Clinically, the patient may present with neurological symptoms such as numbness, weakness, loss of reflexes, or even sudden or progressive paralysis. The affected portion of the body will correlate to where the lesion lies within the spinal cord. The disease typically has an insidious onset, but
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will serve as a superior imaging technique to visualize the extent of the arteriovenous malformation within the cord and may be especially useful if surgical treatment is attempted.
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may be used acutely to help slow the progression of symptoms or they may be used chronically in a poor surgical candidate. In either case,
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Mishra R, Kaw R (May 2005). "Foix–Alajouanine syndrome: an uncommon cause of myelopathy from an anatomic variant circulation".
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symptoms may manifest suddenly. A thorough physical exam may lead a physician toward targeted imaging, with
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will be an important part of the recovery process in helping the patient regain strength and coordination.
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The patients can present with symptoms indicating spinal cord involvement such as (
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T2 weighted MRI showing an arteriovenous malformation indicated by the cursor
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Familial osteosclerosis with abnormalities of the nervous system and meninges
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being the most appropriate imaging modality for initial diagnosis. A spinal
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Spinal muscular atrophy with lower extremity predominance (SMALED)
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Krishnan, Prasad; Banerjee, TapasKumar; Saha, Manash (2013).
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of arms and legs, numbness and loss of sensation and
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degeneration 1142:For more detailed coverage, see 1120:For more detailed coverage, see 1091:For more detailed coverage, see 1057:For more detailed coverage, see 1008:For more detailed coverage, see 1633:Anterior spinal artery syndrome 1: 1435:Amyotrophic lateral sclerosis 1320:Hereditary spastic paraplegia 1178:Normal pressure hydrocephalus 1581:Tropical spastic paraparesis 1404:Progressive muscular atrophy 77:, is a disease caused by an 914:Primary progressive aphasia 327:"Foix-Alajouanine Syndrome" 188:"Foix-Alajouanine syndrome" 1682: 1236:Hashimoto's encephalopathy 942:Posterior cortical atrophy 763:Striatonigral degeneration 614:Cavernous sinus thrombosis 302:"Foix-Alajouanine disease" 148:arteriovenous malformation 117:death in the spinal cord. 79:arteriovenous malformation 1638:Foix–Alajouanine syndrome 1342:Spinal muscular atrophies 1310:Primary lateral sclerosis 1168:Intracranial hypertension 948:Creutzfeldt–Jakob disease 144:endovascular embolization 71:Foix–Alajouanine syndrome 43: 34: 22:Foix–Alajouanine syndrome 1409:Progressive bulbar palsy 1200:Intracranial hypotension 1183:Choroid plexus papilloma 597:Herpesviral encephalitis 382:10.4103/2224-4018.135603 269:10.4103/0972-2327.116931 111:pathological examination 1533:Posterior cord syndrome 1512:Spinal cord compression 921:Frontotemporal dementia 607:Encephalitis lethargica 150:within the spinal cord. 1538:Anterior cord syndrome 1528:Brown-Séquard syndrome 1226:Hepatic encephalopathy 1661:Spinal cord disorders 1569:Demyelinating disease 1548:Cauda equina syndrome 1543:Central cord syndrome 1486:Focal lesions of the 1284:Ataxia–telangiectasia 1241:Static encephalopathy 964:Mitochondrial disease 802:Spasmodic torticollis 712:Basal ganglia disease 113:reveals disseminated 91:Théophile Alajouanine 1231:Toxic encephalopathy 937:Lewy bodies dementia 325:Palmer, Cheryl Ann. 1628:Vascular myelopathy 1574:Transverse myelitis 1279:Friedreich's ataxia 662:Meningoencephalitis 602:Limbic encephalitis 168:Vascular myelopathy 146:or ligation of the 1315:Pseudobulbar palsy 1053:Status epilepticus 1004:Multiple sclerosis 841:Myoclonic epilepsy 704:movement disorders 650:Acute disseminated 592:Viral encephalitis 465:External resources 306:www.whonamedit.com 109:dysfunction), and 97:Signs and symptoms 1648: 1647: 1601:Morvan's syndrome 1453: 1452: 1449: 1448: 1445: 1444: 1249: 1248: 1154: 1153: 1093:Template:Headache 1059:Template:Epilepsy 980: 979: 954:Vascular dementia 797:Status dystonicus 670: 669: 645:Encephalomyelitis 499: 498: 68: 67: 16:Medical condition 1673: 1586:Epidural abscess 1480: 1473: 1466: 1457: 1267: 1258: 1216:Brain herniation 1027: 867:Intention tremor 862:Essential tremor 727:Postencephalitic 695: 686: 575: 556:Diseases of the 550: 543: 536: 527: 399: 387: 386: 384: 360: 354: 353: 341: 335: 334: 322: 316: 315: 313: 312: 298: 292: 291: 281: 271: 247: 241: 240: 204: 198: 197: 184: 156:physical therapy 64: 63: 39: 19: 1681: 1680: 1676: 1675: 1674: 1672: 1671: 1670: 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Retrieved 305: 296: 259: 255: 245: 215:(5): 567–9. 212: 208: 202: 191: 182: 141: 124: 100: 87:Charles Foix 74: 70: 69: 1521:By location 1488:spinal cord 1414:Fazio–Londe 1254:Both/either 1048:Generalised 907:Early-onset 902:Alzheimer's 637:spinal cord 83:spinal cord 27:Other names 1655:Categories 1502:Myelopathy 1022:paroxysmal 994:Autoimmune 787:Dyskinesia 657:Meningitis 635:Brain and 311:2022-04-12 174:References 115:nerve cell 1019:Episodic/ 897:Tauopathy 848:Akathisia 836:Myoclonus 819:Athetosis 751:Tauopathy 516:synd/1755 505:synd/1526 474:eMedicine 138:Treatment 121:Diagnosis 107:sphincter 103:paralysis 55:Neurology 50:Specialty 1507:Myelitis 1385:SMALED2B 1380:SMALED2A 1077:Migraine 1069:Headache 1035:epilepsy 1031:Seizures 889:Dementia 792:Dystonia 485:Orphanet 350:Medscape 331:Medscape 288:24101838 237:41113400 229:15954517 193:Orphanet 162:See also 1495:General 1397:SMA-PME 1392:SMA-PCH 1375:SMALED1 1087:Tension 1082:Cluster 807:Meige's 624:Amoebic 425:8A45.21 279:3788302 81:of the 1116:Stroke 930:Pick's 857:Tremor 824:Chorea 286:  276:  235:  227:  57:  1564:Polio 1557:Other 1430:both: 1362:DSMA1 1357:SMAX2 1352:SMAX1 1332:only: 1305:only: 1209:Other 1131:Other 1043:Focal 676:Brain 579:Brain 490:79093 455:336.1 440:G37.4 233:S2CID 1033:and 744:PKAN 739:NBIA 450:9-CM 284:PMID 225:PMID 89:and 1347:SMA 1330:LMN 1303:UMN 1294:MND 1160:CSF 1111:TIA 756:PSP 732:NMS 701:and 562:CNS 519:at 508:at 446:ICD 431:ICD 416:ICD 377:doi 274:PMC 264:doi 217:doi 132:MRA 128:MRI 1657:: 1271:SA 778:OA 773:HD 722:PD 488:: 477:: 453:: 438:: 435:10 423:: 420:11 371:. 367:. 348:. 329:. 304:. 282:. 272:. 260:16 258:. 254:. 231:. 223:. 213:98 211:. 190:. 1479:e 1472:t 1465:v 923:/ 678:/ 549:e 542:t 535:v 448:- 433:- 418:- 408:D 385:. 379:: 373:2 352:. 333:. 314:. 290:. 266:: 239:. 219:: 196:.

Index


Specialty
Neurology
Edit this on Wikidata
arteriovenous malformation
spinal cord
Charles Foix
Théophile Alajouanine
paralysis
sphincter
pathological examination
nerve cell
MRI
MRA
endovascular embolization
arteriovenous malformation
Corticosteroids
physical therapy
Vascular myelopathy
"Foix-Alajouanine syndrome"
Orphanet
doi
10.1097/01.SMJ.0000154409.48800.43
PMID
15954517
S2CID
41113400
"Congestive myelopathy (Foix-Alajouanine Syndrome) due to intradural arteriovenous fistula of the filum terminale fed by anterior spinal artery: Case report and review of literature"
doi
10.4103/0972-2327.116931

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