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Hypsarrhythmia

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37: 51:. In it high amplitude waves and spikes are present, randomly appearing and with no topographical distribution identified; also, there is no frequency nor amplitude gradient, indicating a highly disorganized brain activity. Although having this seemingly chaotic EEG, the patient didn't show any clinical seizures while being recorded. 92:
Gibbs and Gibbs described hypsarrhythmia (originally spelled with one 'r') in 1952 as "...random high voltage waves and spikes. These spikes vary from moment to moment, both in time and in location. At time they appear to be focal, and a few seconds later they seem to originate from multiple foci.
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Hypsarrhythmia with increased interhemispheric synchronization. Characterized by symmetric and synchronized activity, seen in patients with longstanding evolution, especially in those with West syndrome that changes to
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is very chaotic and disorganized brain electrical activity with no recognizable pattern, whereas a normal brain electrical activity shows clear separation between each signal and visible pattern. It is an abnormal
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Occasionally the spike discharge becomes generalized, but it never appears as a rhythmically repetitive and highly organized pattern that could be confused with a discharge of the
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Vanhatalo S, Somer M, Barth PG (April 2002). "Dutch patients with progressive encephalopathy with edema, hypsarrhythmia, and optic atrophy (PEHO) syndrome".
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A comparison of an awake, resting (with activity), normal EEG with a hypsarrhythmia EEG. The hypsarrhythmia EEG is from a 4-month old girl with
138:(NREM) sleep. When the episodes of voltage attenuation appear at the same time as an epileptic spasm does, they are called electrodecrements. 611: 744: 405: 674: 116:
Through the use of video EEG and continuous monitoring, five variants of the "classical" hypsarrhythmic pattern have been identified:
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Asymmetric hypsarrhythmia. Associated with a brain structural abnormality, and does not necessarily predict the affected hemisphere.
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pattern, consisting of high amplitude and irregular waves and spikes in a background of chaotic and disorganized activity seen on
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In most cases of infantile spasms, hypsarrhythmia either disappears or improves during a cluster of spasms and/or
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Hrachovy, RA; Frost JD (2003). "Infantile epileptic encephalopathy with hypsarrhythmia".
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Hypsarrhythmia with episodes of voltage attenuation. Commonly seen during
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sleep. Hypsarrhythmia rarely persists beyond the age of 24 months.
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Hypsarrhythmia with a consistent focus of abnormal discharge.
81:(EEG), and frequently encountered in infants diagnosed with 320:"EEG in Common Epilepsy Syndromes: eMedicine Neurology" 156:, hypsarrhythmia is one of the diagnostic criteria for 85:, although it can be found in other conditions such as 355: 773: 737: 683: 660: 602: 536: 527: 504: 473: 432: 359: 141:
Hypsarrhythmia with little spike or sharp activity.
55: 26: 21: 406: 8: 152:Together with developmental regression and 533: 413: 399: 391: 356: 35: 18: 202: 781:Citizens United for Research in Epilepsy 169: 336: 325: 177:Millichap, JJ; Millichap, JG (2015). 7: 698:Dentatorubral–pallidoluysian atrophy 745:Sudden unexpected death in epilepsy 243:Journal of Clinical Neurophysiology 230:. Cambridge, Mass.: Addison-Wesley. 675:Complex partial status epilepticus 179:"Hypsarhythmia or Hypsarrhythmia?" 14: 760:Psychogenic non-epileptic seizure 632:Benign familial neonatal seizures 584:Sleep-related hypermotor epilepsy 255:10.1097/00004691-200311000-00004 228:Atlas of electroencephalography 720:Early myoclonic encephalopathy 693:Progressive myoclonus epilepsy 1: 195:10.15844/pedneurbriefs-29-8-7 670:Epilepsia partialis continua 725:Juvenile myoclonic epilepsy 703:Unverricht–Lundborg disease 149:stands for hypsarrhythmia. 858: 642:Myoclonic astatic epilepsy 183:Pediatric Neurology Briefs 793:Epilepsy Action Australia 43: 34: 755:Landau–Kleffner syndrome 589:Panayiotopoulos syndrome 637:Lennox–Gastaut syndrome 519:Epilepsy and employment 123:Lennox-Gastaut syndrome 30:From Greek Hyps= Height 842:Neurological disorders 837:Electroencephalography 569:Temporal lobe epilepsy 489:Electroencephalography 335:Cite journal requires 574:Frontal lobe epilepsy 136:nonrapid eye movement 810:Epilepsy Research UK 594:Vertiginous epilepsy 514:Epilepsy and driving 465:Epilepsy in children 298:10.1055/s-2002-32371 79:electroencephalogram 798:Epilepsy Foundation 765:Epilepsy in animals 445:Aura (warning sign) 685:Myoclonic epilepsy 662:Status epilepticus 226:Gibbs, FA (1952). 87:tuberous sclerosis 824: 823: 738:Related disorders 733: 732: 579:Rolandic epilepsy 388: 387: 67: 66: 16:Medical condition 849: 815:Epilepsy Society 804:Epilepsy Outlook 647:Epileptic spasms 559:Gelastic seizure 534: 460:Neonatal seizure 415: 408: 401: 392: 357: 345: 344: 338: 333: 331: 323: 316: 310: 309: 281: 275: 274: 238: 232: 231: 223: 217: 216: 206: 174: 154:infantile spasms 83:infantile spasms 39: 19: 857: 856: 852: 851: 850: 848: 847: 846: 827: 826: 825: 820: 787:Epilepsy Action 769: 729: 679: 656: 652:Febrile seizure 617:Absence seizure 598: 554:Complex partial 523: 506:Personal issues 500: 485:Investigations 481:Anticonvulsants 469: 455:Epileptogenesis 450:Postictal state 428: 419: 389: 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213:26933601 379:D013036 204:4747135 433:Basics 304:  269:  261:  211:  201:  538:Focal 267:S2CID 817:(UK) 806:(UK) 800:(US) 789:(UK) 783:(US) 424:and 374:MeSH 341:help 302:PMID 259:PMID 209:PMID 294:doi 251:doi 199:PMC 191:doi 106:REM 97:or 833:: 377:: 332:: 330:}} 326:{{ 300:. 290:33 288:. 265:. 257:. 247:20 245:. 207:. 197:. 187:29 185:. 181:. 160:. 89:. 414:e 407:t 400:v 366:D 343:) 339:( 308:. 296:: 273:. 253:: 215:. 193:: 125:.

Index


cryptogenic
West syndrome
Specialty
Neurology
interictal
electroencephalogram
infantile spasms
tuberous sclerosis
REM
Lennox-Gastaut syndrome
nonrapid eye movement
PEHO syndrome
infantile spasms
West syndrome
"Hypsarhythmia or Hypsarrhythmia?"
doi
10.15844/pedneurbriefs-29-8-7
PMC
4747135
PMID
26933601
doi
10.1097/00004691-200311000-00004
PMID
14734931
S2CID
39542946
doi
10.1055/s-2002-32371

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