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It is a rare developmental disorder that affects maxilla, also known as the upper jaw in most vertebrates. The disorder is often diagnosed in early childhood. Since its original description as hemimaxillofacial dysplasia by doctors in 1987, less than 40 cases have been reported in the
English
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All cases reported appear to represent sporadic occurrence. There is no specific inheritance pattern. The male-to-female ratio of affected is 1.8:1 and is often diagnosed before the age of 9. The disorder affects the right and left sides of the maxilla almost equally.
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Miles DA, Lovas JL, Cohen MM., Jr
Hemimaxillofacial dysplasia: A newly recognized disorder of facial asymmetry, hypertrichosis of the facial skin, unilateral enlargement of the maxilla, and hypoplastic teeth in two patients. Oral Surg Oral Med Oral Pathol.
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Paticoff K, Marion RW, Shprintzen RJ, Shanske AL, Eisig SB. Hemimaxillofacial dysplasia: A report of two new cases and further delineation of the disorder. Oral Surg Oral Med Oral Pathol Oral Radiol Endod.
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Danforth RA, Melrose RJ, Abrams AM, Handlers JP. Segmental odontomaxillary dysplasia. Report of eight cases and comparison with hemimaxillofacial dysplasia. Oral Surg Oral Med Oral Pathol. 1990;70:81–5.
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Packota GV, Pharoah MJ, Petrikowski CG. Radiographic features of segmental odontomaxillary dysplasia: A study of 12 cases. Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 1996;82:577–84.
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Prusack N, Pringle G, Scotti V, Chen SY. Segmental odontomaxillary dysplasia: a case report and review of the literature. Oral Surg Oral Med Oral Pathol Oral Radiol Endod. 2000;90:483–8.
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DeSalvo MS, Copete MA, Riesenberger RE, Cleveland DB, Chen SY. Segmental odontomaxillary dysplasia (hemimaxillofacial dysplasia): Case report. Pediatr Dent.1996;18:154–6.
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Becktor KB, Reibel J, Vedel B, Kjaer I. Segmental odontomaxillary dysplasia: Clinical, radiological and histological aspects of four cases. Oral Dis. 2002;8:106–10.
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Welsch MJ, Stein SL. A syndrome of hemimaxillary enlargement, asymmetry of the face, tooth abnormalities, and skin findings (HATS) Pediatr
Dermatol. 2004;21:448–51
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Armstrong C, Napier SS, Boyd RC, Gregg TA. Histopathology of the teeth in segmental odontomaxillary dysplasia: new findings. J Oral Pathol Med. 2004;33:246–8.
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Jones AC, Ford MJ. Simultaneous occurrence of segmental odontomaxillary dysplasia and Becker's nevus. J Oral
Maxillofac Surg. 1999;57:1251–4.
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Shah, Ajaz; Latoo, Suhail; Ahmed, Irshad; Malik, Altaf H.; Hassan, Shahid; Bhat, Abraar; Mir, Shazia; Jain, Nitul (2012-01-01).
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Drake DL. Segmental odontomaxillary dysplasia: an unusual orthodontic challenge. Am J Orthod
Dentofacial Orthop. 2003;123:84–6.
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23:. The cause is unknown, and the disease affects the jaws, teeth, and adjacent soft tissue. The
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31:(baby teeth) may be smaller than usual. It is a relatively recent discovery.
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Kahn, Michael A. Basic Oral and
Maxillofacial Pathology. Volume 1. 2001.
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Gavalda C. Segmental odontomaxillary dysplasia. Med Oral. 2004;9:181.
78:"Midline segmental odontomaxillary dysplasia"
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27:may be congenitally missing, and the
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